coexistant of fabry disease and iga glomerulonephritis in a 39 year old male

نویسندگان

atieh makhlough

seyyedeh fatemeh emadi tarkami

چکیده

anderson-fabry disease is a rare inherited x-linked lysosomal storage disease caused by deficiency of the enzyme alpha-galactosidase a. hereby we report a 39 year old male that presented with proteinuria and edema. histopathologic, immunofluorescence and ultrastractural examination of renal tissue were in favor  of  fabry disease in associate with iga nephropathy. fabry's disease associated with iga nephropathy apparently is extremely rare, and the present case is among few reported cases in literature.

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عنوان ژورنال:
iranian journal of pathology

ناشر: iranian society of pathology

ISSN 1735-5303

دوره 4

شماره 2 2009

کلمات کلیدی

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